{"id":125439,"date":"2019-09-19T11:50:50","date_gmt":"2020-04-21T02:07:58","guid":{"rendered":"http:\/\/www.05921.net\/index.php\/125439\/"},"modified":"2020-04-21T10:08:01","modified_gmt":"2020-04-21T02:08:01","slug":"a49e39e0ee","status":"publish","type":"post","link":"https:\/\/www.05921.net\/index.php\/125439\/","title":{"rendered":"\u300c\u8774\u8776\u5b9d\u8d1d\u300d\u75c5\u4f8b\u5206\u4eab\uff0c\u4eba\u7c7b\u7f55\u89c1\u75c5\u4e2d\u6700\u75db\u82e6\u7684\u75be\u75c5\u4e4b\u4e00"},"content":{"rendered":"
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\"\u300c\u8774\u8776\u5b9d\u8d1d\u300d\u75c5\u4f8b\u5206\u4eab\uff0c\u4eba\u7c7b\u7f55\u89c1\u75c5\u4e2d\u6700\u75db\u82e6\u7684\u75be\u75c5\u4e4b\u4e00\"<\/section>\n

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\u75c5\u4f8b\u6982\u51b5<\/span><\/strong><\/span><\/span><\/section>\n
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\u60a3\u8005\u6027\u522b\uff1a<\/span><\/strong>\u5973<\/span><\/section>\n
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\u60a3\u8005\u5e74\u9f84\uff1a<\/span><\/strong>19 \u5c81<\/span><\/section>\n
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\u73b0\u75c5\u53f2\uff1a<\/span><\/strong><\/span><\/section>\n
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\u51fa\u751f\u540e\u8eab\u4e0a\u5373\u51fa\u73b0\u6c34\u75b1\uff0c\u540e\u591a\u56e0\u673a\u68b0\u78b0\u89e6\u9891\u7e41\u518d\u53d1\uff0c\u4f34\u7619\u75d2\uff0c\u6414\u6293\u540e\u52a0\u91cd\u3002<\/span><\/section>\n
 <\/span><\/section>\n
\u67e5\u4f53\u5168\u8eab\u53ef\u53ca\u7cdc\u70c2\u9762\u3001\u7ed3\u75c2\u3001\u840e\u7f29\u53ca\u7622\u75d5\uff0c\u4ee5\u56db\u80a2\u4f38\u4fa7\u4e3a\u91cd\uff0c\u5173\u8282\u90e8\u4f4d\u663e\u8457\uff0c\u6307\u7532\u53ef\u89c1\u589e\u539a\u3001\u53d8\u5f62\u3001\u8131\u843d\u3002<\/span><\/section>\n

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<\/section>\n
\u75c5\u4f8b\u8bca\u65ad\uff1a<\/span><\/strong>\u9690\u6027\u8425\u517b\u4e0d\u826f\u578b\u5927\u75b1\u6027\u8868\u76ae\u677e\u89e3\u75c7<\/span><\/section>\n
 <\/span><\/section>\n
\u75c5\u4f8b\u56fe\u7247\uff1a<\/span><\/strong><\/span><\/section>\n
 <\/span><\/section>\n
\"\u300c\u8774\u8776\u5b9d\u8d1d\u300d\u75c5\u4f8b\u5206\u4eab\uff0c\u4eba\u7c7b\u7f55\u89c1\u75c5\u4e2d\u6700\u75db\u82e6\u7684\u75be\u75c5\u4e4b\u4e00\"<\/section>\n
<\/span>\u75c5\u4f8b\u56fe\u7247\u6765\u6e90\uff1a\u9648\u4e07\u946b<\/span>
<\/section>\n


<\/p>\n

\u8fd9\u662f\u5728<\/span>\u667a\u80fd\u76ae\u80a4\u300c 2019 \u9996\u5c4a\u5168\u56fd\u76ae\u80a4\u75c5\u4f8b\u4ea4\u6d41\u5927\u8d5b\u300d<\/span>\u4e2d\uff0c\u533b\u751f\u5206\u4eab\u7684\u4e00\u4f8b\u4e34\u5e8a\u75c5\u4f8b\u3002<\/span><\/section>\n

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<\/section>\n
\u2192 \u70b9\u51fb\u67e5\u770b\u75c5\u4f8b\u8be6\u60c5<\/span><\/a><\/section>\n

<\/section>\n
\u5927\u8d5b\u671f\u95f4\uff0c\u533b\u751f\u5728\u4ea4\u6d41\u5708\u5185\u5206\u4eab\u7684\u75c5\u4f8b\uff0c\u6bcf\u5468\u90fd\u4f1a\u9080\u8bf7\u4e13\u5bb6\u8fdb\u884c\u70b9\u8bc4\u3002\u8fd9\u671f\u75c5\u4f8b\uff0c\u5c31\u83b7\u5f97\u4e86<\/span>\u798f\u5efa\u533b\u79d1\u5927\u5b66\u9644\u5c5e\u7b2c\u4e00\u533b\u9662\u76ae\u80a4\u79d1\u526f\u4e3b\u4efb\u533b\u5e08 \u7eaa\u8d85\u526f\u6559\u6388<\/strong><\/span> \u7684\u70b9\u8bc4\u3002<\/span><\/section>\n

<\/span><\/section>\n
<\/section>\n
\u6559\u6388\u8868\u793a\uff1a\u8fd8\u9700\u8981\u52a0\u5165\u75c5\u7406\u53ca\u514d\u75ab\u8367\u5149\u67d3\u8272\u8bca\u65ad\u786e\u8bca\uff0c\u4f46\u672c\u75c5\u4f8b\u662f\u4e00\u4f8b\u4e34\u5e8a\u8f83\u4e3a\u7ecf\u5178\u7684<\/span>\u8425\u517b\u4e0d\u826f\u6027\u5927\u75b1\u6027\u8868\u76ae\u677e\u89e3\u75c7(dystrophic EB,DEB)\u3002<\/span><\/section>\n

<\/span><\/section>\n
<\/section>\n
 <\/span>\u2192 \u70b9\u51fb\u67e5\u770b\u4e13\u5bb6\u70b9\u8bc4<\/span><\/a><\/section>\n
 <\/span><\/section>\n
 <\/span><\/section>\n
\u4e07\u5206\u4e4b\u4e00\u7684\u300c\u7f8e\u4e3d\u8106\u5f31\u300d<\/span><\/strong><\/span><\/span><\/span><\/section>\n
 <\/span><\/section>\n
DEB \u662f\u5148\u5929\u6027\u5927\u75b1\u6027\u8868\u76ae\u677e\u89e3\u75c7\uff08epidermolysis bullosa EB\uff09\u7684\u4e00\u79cd\u7c7b\u578b\u3002<\/span><\/section>\n
<\/section>\n
\u5927\u75b1\u6027\u8868\u76ae\u677e\u89e3\u75c7\u5206\u4e3a<\/span>\u5148\u5929\u6027<\/span>\uff08\u9057\u4f20\u6027\uff09<\/span>\u548c<\/span>\u83b7\u5f97\u6027<\/span>\uff08epidermolysis bullosa acquisita EBA\uff09\u4e24\u79cd\u3002<\/span><\/section>\n
 <\/span><\/section>\n
\u5176\u4e2d\uff0c\u5148\u5929\u6027\u53c8\u6839\u636e\u6c34\u75b1\u88c2\u9699\u7684\u4e0d\u540c\u4f4d\u7f6e\uff0c\u5206\u4e3a 4 \u79cd\u7c7b\u578b:<\/span><\/section>\n
 <\/span><\/section>\n
\"\u300c\u8774\u8776\u5b9d\u8d1d\u300d\u75c5\u4f8b\u5206\u4eab\uff0c\u4eba\u7c7b\u7f55\u89c1\u75c5\u4e2d\u6700\u75db\u82e6\u7684\u75be\u75c5\u4e4b\u4e00\"<\/section>\n
 <\/span>
<\/section>\n
\u90fd\u662f\u7531\u4e8e\u7f16\u7801\u89d2\u86cb\u767d\u6216\u76ae\u80a4\u57fa\u5e95\u819c\u5e26<\/span>\uff08basement membrane zone ,BMZ\uff09<\/span>\u7684\u57fa\u56e0\u7a81\u53d8\u5bfc\u81f4<\/span>\u3002<\/span>\u4e34\u5e8a EB \u7684\u5171\u540c\u7279\u70b9\u662f\u76ae\u80a4\u5728\u53d7\u5230\u8f7b\u5fae\u6469\u64e6\u6216\u78b0\u649e\u540e\u51fa\u73b0\u6c34\u75b1\u53ca\u8840\u75b1\uff0c\u597d\u53d1\u4e8e\u80a2\u7aef\u53ca\u56db\u80a2\u5173\u8282\u4f38\u4fa7<\/span>\u3002\u76ae\u635f\u6108\u5408\u540e\u53ef\u5f62\u6210\u7622\u75d5\u6216\u7c9f\u4e18\u75b9\uff0c\u53cd\u590d\u53d1\u4f5c\u53ef\u4f7f\u7532\u8131\u843d\u3002\u8425\u517b\u4e0d\u826f\u578b\u7684\u5e38\u5728\u51fa\u751f\u540e\u51fa\u73b0\u76ae\u75b9\uff0c\u7d2f\u53ca\u9ecf\u819c\u3002<\/span><\/section>\n

<\/span><\/section>\n
<\/section>\n
\u60a3\u6709\u5148\u5929\u6027\u5927\u75b1\u6027\u8868\u76ae\u677e\u89e3\u75c7\u7684\u60a3\u8005\uff0c\u6709\u4e2a\u7f8e\u4e3d\u7684\u540d\u5b57\u300c\u8774\u8776\u5b9d\u8d1d\u300d\u3002\u4f46\u4ed6\u4eec\u6240\u60a3\u7684\u662f\u4eba\u7c7b\u7f55\u89c1\u75c5\u4e2d\u516c\u8ba4\u6700\u75db\u82e6\u7684\u75be\u75c5\u4e4b\u4e00\uff0c<\/span>\u76ae\u80a4\u50cf\u8774\u8776\u7fc5\u8180\u4e00\u6837\u8106\u5f31\uff0c\u800c\u4e14\u76ee\u524d\u6ca1\u6709\u5b89\u5168\u6709\u6548\u7684\u6839\u6cbb\u65b9\u6cd5<\/span>\u3002<\/span><\/section>\n
 <\/span><\/section>\n
\u521d\u751f\u5a74\u513f\u663e\u6027\u9057\u4f20\u578b\u53d1\u75c5\u7387\u4e3a 1:50000\uff0c\u4e25\u91cd\u9690\u6027\u9057\u4f20\u578b\u4e3a 1:200000\uff5e1:500000\u3002[1]<\/span>\u636e\u6b64\u4f30\u7b97\uff0c<\/span>\u4e2d\u56fd\u7684 EB \u60a3\u8005\u5df2\u7ecf\u8fc7\u4e07\u4eba\u3002<\/span><\/span><\/section>\n
 <\/span><\/section>\n
 <\/span><\/section>\n
\u8fd9\u662f\u4e00\u79cd\u53ef\u80fd\u7ec8\u8eab\u75db\u82e6\u7684\u75be\u75c5<\/span><\/strong><\/span><\/span><\/section>\n
 <\/span><\/section>\n
\u300c\u8fd9\u662f\u4e00\u79cd\u7ec8\u751f\u75db\u82e6\u7684\u75be\u75c5\u3002\u300d\u5317\u4eac\u5927\u5b66\u7b2c\u4e00\u533b\u9662\u76ae\u80a4\u79d1\u526f\u4e3b\u4efb\u533b\u5e08\u6797\u5fd7\u6dfc\u533b\u751f\uff0c\u5728\u300a\u4e2d\u56fd\u9752\u5e74\u62a5\u300b\u7684\u76f8\u5173\u62a5\u9053\u4e2d\u8868\u793a\u3002\u65e5\u5e38\u751f\u6d3b\u7684\u6bcf\u4e00\u4e2a\u52a8\u4f5c\u90fd\u6709\u53ef\u80fd\u7ed9\u4ed6\u4eec\u5e26\u6765\u5267\u70c8\u75bc\u75db\u3002\u6bd4\u5982\u8863\u670d\u7684\u6807\u7b7e\u5982\u679c\u4e0d\u53ca\u65f6\u62c6\u9664\uff0c\u5c31\u53ef\u80fd\u4f1a\u6469\u64e6\u5bfc\u81f4\u60a3\u8005\u9888\u90e8\u51fa\u73b0\u6c34\u75b1\u3002<\/span><\/section>\n
 <\/span><\/section>\n
EB \u7684\u9884\u540e\uff0c\u4e5f\u662f\u5f88\u591a\u533b\u751f\u8ba4\u4e3a\uff0c\u8ddf\u60a3\u8005\u53ca\u5bb6\u5c5e\u6c9f\u901a\u6700\u96be\u7684\u5730\u65b9<\/strong><\/span>\u3002<\/span><\/section>\n
 <\/span><\/section>\n
\u9884\u540e\u5dee\u5f02\u8f83\u5927\uff0c\u53d6\u51b3\u4e8e\u5148\u5929\u6027\u5927\u75b1\u6027\u8868\u76ae\u677e\u89e3\u75c7\u4e9a\u578b\u548c\u60a3\u8005\u7684\u5065\u5eb7\u72b6\u51b5\u3002\u8f7b\u578b\u5148\u5929\u6027\u5927\u75b1\u6027\u8868\u76ae\u677e\u89e3\u75c7\u968f\u5e74\u9f84\u589e\u52a0\u75c7\u72b6\u4f1a\u5f97\u5230\u6539\u5584\uff0c\u91cd\u578b\u60a3\u8005\u5f88\u53ef\u80fd\u51fa\u73b0\u5404\u79cd\u4e25\u91cd\u5e76\u53d1\u75c7\uff0c\u591a\u6570\u4e25\u91cd\u5a01\u80c1\u60a3\u8005\u529f\u80fd\u53ca\u5f71\u54cd\u5bff\u547d\u3002\u6781\u91cd\u578b\u60a3\u8005\u5e38\u5728\u5a74\u5e7c\u513f\u671f\u6b7b\u4ea1\u3002<\/span><\/section>\n
 <\/span><\/section>\n
 <\/span><\/section>\n
\u6211\u4eec\u8fd8\u80fd\u505a\u4ec0\u4e48\uff1f<\/span><\/strong><\/span><\/span><\/section>\n
 <\/span><\/section>\n
\u7531\u4e8e\u53d1\u75c5\u7387\u4f4e\uff0c\u60a3\u8005\u57fa\u6570\u5c0f\uff0c\u53d7\u73b0\u884c\u533b\u7597\u6c34\u5e73\u6240\u9650\uff0c\u5927\u90e8\u5206 EB \u60a3\u8005\u90fd\u9762\u4e34\u56e0\u8bca\u65ad\u4e0d\u660e\u786e\u3001\u8bef\u8bca\u7ee7\u800c\u8f97\u8f6c\u5f02\u5730\u5c31\u533b\u7684\u5904\u5883\uff0c\u77ed\u5219\u51e0\u4e2a\u6708\uff0c\u957f\u5219\u51e0\u5e74\uff0c\u9519\u8fc7\u6700\u4f73\u6cbb\u7597\u671f\u3002<\/span><\/section>\n
 <\/span><\/section>\n
\u56e0\u6b64\uff0c\u5bf9\u4e8e\u5f88\u591a EB \u60a3\u8005\u6765\u8bb2\uff0c\u65e9\u4e00\u6b65\u7684\u786e\u8bca\uff0c\u90fd\u610f\u5473\u7740\u66f4\u8fdb\u4e00\u6b65\u7684\u5e0c\u671b\u3002<\/span><\/section>\n

<\/span><\/section>\n
<\/section>\n
\u667a\u80fd\u76ae\u80a4\u4e3e\u529e\u672c\u6b21\u75c5\u4f8b\u4ea4\u6d41\u5927\u8d5b\u7684\u521d\u8877\uff0c\u4e5f\u662f<\/span>\u5e0c\u671b\u4fc3\u8fdb\u4e34\u5e8a\u533b\u5e08\u5bf9\u5404\u7c7b\u76ae\u80a4\u75c5\u7684\u4ea4\u6d41\u548c\u5b66\u4e60\uff0c\u534f\u52a9\u533b\u5e08\u5206\u4eab\u66f4\u591a\u7684\u8bca\u7597\u75c5\u4f8b\u548c\u7ecf\u9a8c<\/span>\u3002<\/span><\/section>\n

<\/span><\/section>\n
<\/section>\n
<\/span> <\/span>\u2192 \u70b9\u6b64\u4ea4\u6d41\u66f4\u591a\u75c5\u4f8b<\/span><\/a><\/section>\n
 <\/span><\/section>\n

\u9488\u5bf9\u4ea4\u6d41\u5708\u5185\u5206\u4eab\u51fa\u7684\u8fd9\u8d77\u75c5\u4f8b\uff0c\u7eaa\u8d85\u6559\u6388\u4e5f\u7ed9\u51fa\u4e86\u76f8\u5173\u6cbb\u7597\u5efa\u8bae\u3002<\/span><\/p>\n


<\/p>\n

    \n
  • \n

    \u4fdd\u62a4\u76ae\u80a4\u3002\u9632\u6b62\u6469\u64e6\u548c\u538b\u8feb\u635f\u4f24\uff0c\u51cf\u5c11\u5e76\u53d1\u75c7\u53d1\u751f\u7387\u5982\u9884\u9632\u611f\u67d3\u7b49\uff0c\u63d0\u9ad8\u60a3\u8005\u751f\u6d3b\u8d28\u91cf\u3002<\/span><\/p>\n<\/li>\n<\/ul>\n

    <\/section>\n


    <\/p>\n

      \n
    • \n

      \u901a\u5e38\u5efa\u8bae\u4f7f\u7528\u65e0\u83cc\u9488\u523a\u7834\u65b0\u7684\u6c34\u75b1\uff0c\u4e0d\u80fd\u62c9\u626f\u6c34\u75b1\u3002<\/span><\/p>\n<\/li>\n<\/ul>\n

      <\/section>\n


      <\/p>\n

        \n
      • \n

        \u56fa\u5b9a\u6577\u6599\u4e0d\u4f7f\u7528\u80f6\u5e03\uff0c\u5efa\u8bae\u4f7f\u7528\u889c\u5b50\uff0c\u68c9\u7ef7\u5e26\u6216\u7ba1\u72b6\u7ef7\u5e26\u3002<\/span><\/p>\n<\/li>\n<\/ul>\n

        <\/section>\n


        <\/p>\n

          \n
        • \n

          \u4f7f\u7528\u975e\u5904\u65b9\u6b62\u75db\u836f\uff0c\u5982\u6251\u70ed\u606f\u75db\u7b49\u300216 \u5c81\u4ee5\u4e0b\u7684\u513f\u7ae5\u4e0d\u5e94\u670d\u7528\u963f\u53f8\u5339\u6797\uff0c\u56e0\u4e3a\u5b83\u53ef\u80fd\u5f15\u53d1\u4e25\u91cd\u7684 Reye \u7efc\u5408\u75c7\u3002<\/span><\/p>\n<\/li>\n<\/ul>\n

          <\/section>\n


          <\/p>\n

          \u76ee\u524d\uff0c\u5df2\u7ecf\u6709\u7814\u7a76\u7684\u6cbb\u7597\u65b9\u5411\u662f\uff0c\u901a\u8fc7\u75c5\u6bd2\u4f5c\u4e3a\u8f7d\u4f53\u91cd\u7ec4\u67d0\u4e9b\u7a81\u53d8\u57fa\u56e0\u7684\u300c\u6821\u6b63\u300d\u7247\u6bb5\uff0c\u5728\u76ae\u80a4\u7684\u6210\u7ea4\u7ef4\u7ec6\u80de\u4f5c\u7528\u8c03\u8282\u4e0b\uff0c\u6700\u7ec8\u4ea7\u751f\u89d2\u86cb\u767d\u6216 BMZ \u8fde\u63a5\u9700\u8981\u7684\u86cb\u767d\uff0c\u4ece\u800c\u6cbb\u6108\u672c\u75c5\u3002\u4f46\u5b83\u53ef\u80fd\u8fd8\u9700\u8981\u51e0\u5e74\u65f6\u95f4\uff0c\u76f4\u5230\u7814\u7a76\u4eba\u5458\u8bc1\u5b9e\u5176\u5b89\u5168\u6709\u6548\u3002<\/span><\/p>\n


          <\/p>\n

          \"\u300c\u8774\u8776\u5b9d\u8d1d\u300d\u75c5\u4f8b\u5206\u4eab\uff0c\u4eba\u7c7b\u7f55\u89c1\u75c5\u4e2d\u6700\u75db\u82e6\u7684\u75be\u75c5\u4e4b\u4e00\"<\/section>\n

          \"\u300c\u8774\u8776\u5b9d\u8d1d\u300d\u75c5\u4f8b\u5206\u4eab\uff0c\u4eba\u7c7b\u7f55\u89c1\u75c5\u4e2d\u6700\u75db\u82e6\u7684\u75be\u75c5\u4e4b\u4e00\"<\/span><\/strong>\u6587\u672b\u70b9\u51fb\u3010\u9605\u8bfb\u539f\u6587\u3011\u8fdb\u5165\u5927\u8d5b\u4ea4\u6d41<\/span><\/strong><\/p>\n

           <\/span><\/section>\n

          <\/section>\n
          \u53c2\u8003\u6587\u732e\uff1a<\/span>\u9773\u57f9\u82f1[1]. \u5927\u75b1\u6027\u8868\u76ae\u677e\u89e3\u75c7[J]. \u4e2d\u534e\u76ae\u80a4\u79d1\u6742\u5fd7, 2004(10).<\/span><\/section>\n
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          <\/span><\/section>\n
          \u58f0\u660e\uff1a\u75c5\u4f8b\u6765\u6e90\u3010\u667a\u80fd\u76ae\u80a4\u533b\u751f\u4ea4\u6d41\u5708\u3011\uff0c\u4ec5\u7528\u4f5c\u533b\u5b66\u4ea4\u6d41\uff0c\u672a\u7ecf\u6388\u6743\u4e25\u7981\u8f6c\u8f7d<\/span><\/section>\n<\/section>\n<\/section><\/div>\n","protected":false},"excerpt":{"rendered":"

          \u75c5\u4f8b\u6982\u51b5   \u60a3\u8005\u6027\u522b\uff1a\u5973   \u60a3\u8005\u5e74\u9f84\uff1a19 \u5c81   \u73b0\u75c5\u53f2\uff1a   […]<\/p>\n","protected":false},"author":1,"featured_media":125440,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":[],"categories":[2],"tags":[],"_links":{"self":[{"href":"https:\/\/www.05921.net\/index.php\/wp-json\/wp\/v2\/posts\/125439"}],"collection":[{"href":"https:\/\/www.05921.net\/index.php\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.05921.net\/index.php\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.05921.net\/index.php\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.05921.net\/index.php\/wp-json\/wp\/v2\/comments?post=125439"}],"version-history":[{"count":1,"href":"https:\/\/www.05921.net\/index.php\/wp-json\/wp\/v2\/posts\/125439\/revisions"}],"predecessor-version":[{"id":125446,"href":"https:\/\/www.05921.net\/index.php\/wp-json\/wp\/v2\/posts\/125439\/revisions\/125446"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/www.05921.net\/index.php\/wp-json\/wp\/v2\/media\/125440"}],"wp:attachment":[{"href":"https:\/\/www.05921.net\/index.php\/wp-json\/wp\/v2\/media?parent=125439"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.05921.net\/index.php\/wp-json\/wp\/v2\/categories?post=125439"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.05921.net\/index.php\/wp-json\/wp\/v2\/tags?post=125439"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}